Table 1.

Biosynthesis Studies of Bone Marrow Erythroblasts and Peripheral Reticulocytes From Patient No. 2

Time (mins)α/β Aα/β Xβ AXα/( βA + β X)
Marrow 
Total counts 2.7 2  0.71 1.2 
Specific activity 2.8 0.24 0.08  
Total counts 2.7 1.7 0.63 1  
Specific activity 2.5 0.23 0.09  
15 
Total counts 2.8 2  0.71 1.1 
Specific activity 2.2 0.22 0.1  
60 
Total counts 2.4 2.1 0.91 1.1 
Specific activity 2  0.13 0.07  
Blood 
Total counts 3.7 2.1 0.59 1.3 
Specific activity 2.7 0.25 0.09  
Total counts 3.7 1.9 0.5 1.2 
Specific activity 3.5 0.18 0.05  
15 
Total counts 4.1 2.3 0.59 1.5 
Specific activity 3.5 0.31 0.09  
60 
Total counts 3.9 3.8 1  1.9 
Specific activity 2.9 0.31 0.11 
Time (mins)α/β Aα/β Xβ AXα/( βA + β X)
Marrow 
Total counts 2.7 2  0.71 1.2 
Specific activity 2.8 0.24 0.08  
Total counts 2.7 1.7 0.63 1  
Specific activity 2.5 0.23 0.09  
15 
Total counts 2.8 2  0.71 1.1 
Specific activity 2.2 0.22 0.1  
60 
Total counts 2.4 2.1 0.91 1.1 
Specific activity 2  0.13 0.07  
Blood 
Total counts 3.7 2.1 0.59 1.3 
Specific activity 2.7 0.25 0.09  
Total counts 3.7 1.9 0.5 1.2 
Specific activity 3.5 0.18 0.05  
15 
Total counts 4.1 2.3 0.59 1.5 
Specific activity 3.5 0.31 0.09  
60 
Total counts 3.9 3.8 1  1.9 
Specific activity 2.9 0.31 0.11 
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