Mean PedsQL scores for IL2RG/JAK3 SCID patients posttransplantation (parent and children report)
| . | UK norm . | IL2RG/JAK3 SCID, mean (P) . | Ongoing immunoglobulin replacement, mean (P) . | No immunoglobulin replacement, mean (P) . | Ongoing medical issues (P) . | No medical issues (P) . |
|---|---|---|---|---|---|---|
| Parent report | N = 19 | N = 8 | N = 11 | N = 12 | N = 7 | |
| Total | 84.6 | 70.9 (.009) | 63.9 (.02) | 75.0 (.06) | 70.0 (.02) | 72.3 (.04) |
| Psychosocial | 82.2 | 66.5 (.007) | 56.5 (.01) | 73.8 (.08) | 64.7 (.01) | 69.5 (.06) |
| Physical | 89.1 | 82.4 (.19) | 77.7 (.12) | 85.8 (.28) | 79.9 (.10) | 86.6 (.37) |
| Emotional | 78.3 | 72.9 (.34) | 60.0 (.06) | 82.3 (.81) | 69.6 (.15) | 78.6 (.52) |
| Social | 86.8 | 77.4 (.13) | 70.0 (.09) | 82.7 (.24) | 77.5 (.15) | 77.1 (.12) |
| School | 81.5 | 63.5 (.02) | 55.3 (.01) | 68.0 (.09) | 58.8 (.01) | 70.2 (.19) |
| Child report | N = 15 | N = 5 | N = 10 | N = 8 | N = 7 | |
| Total | 83.9 | 77.8 (.23) | 71.7 (.16) | 80.8 (.28) | 77.6 (.23) | 77.9 (.17) |
| Psychosocial | 81.8 | 74.1 (.17) | 67.3 (.13) | 77.5 (.23) | 75.2 (.23) | 72.9 (.12) |
| Physical | 88.5 | 84.6 (.45) | 80.0 (.23) | 86.9 (.33) | 82.0 (.24) | 87.5 (.42) |
| Emotional | 78.5 | 79.3 (.89) | 67.0 (.24) | 85.5 (.88) | 75.0 (.37) | 84.3 (.79) |
| Social | 87.7 | 75.7 (.09) | 77.0 (.17) | 75.0 (.09) | 81.3 (.21) | 69.3 (.08) |
| School | 78.9 | 67.3 (.08) | 58.0 (.05) | 72.0 (.19) | 69.4 (.15) | 65.0 (.09) |
| . | UK norm . | IL2RG/JAK3 SCID, mean (P) . | Ongoing immunoglobulin replacement, mean (P) . | No immunoglobulin replacement, mean (P) . | Ongoing medical issues (P) . | No medical issues (P) . |
|---|---|---|---|---|---|---|
| Parent report | N = 19 | N = 8 | N = 11 | N = 12 | N = 7 | |
| Total | 84.6 | 70.9 (.009) | 63.9 (.02) | 75.0 (.06) | 70.0 (.02) | 72.3 (.04) |
| Psychosocial | 82.2 | 66.5 (.007) | 56.5 (.01) | 73.8 (.08) | 64.7 (.01) | 69.5 (.06) |
| Physical | 89.1 | 82.4 (.19) | 77.7 (.12) | 85.8 (.28) | 79.9 (.10) | 86.6 (.37) |
| Emotional | 78.3 | 72.9 (.34) | 60.0 (.06) | 82.3 (.81) | 69.6 (.15) | 78.6 (.52) |
| Social | 86.8 | 77.4 (.13) | 70.0 (.09) | 82.7 (.24) | 77.5 (.15) | 77.1 (.12) |
| School | 81.5 | 63.5 (.02) | 55.3 (.01) | 68.0 (.09) | 58.8 (.01) | 70.2 (.19) |
| Child report | N = 15 | N = 5 | N = 10 | N = 8 | N = 7 | |
| Total | 83.9 | 77.8 (.23) | 71.7 (.16) | 80.8 (.28) | 77.6 (.23) | 77.9 (.17) |
| Psychosocial | 81.8 | 74.1 (.17) | 67.3 (.13) | 77.5 (.23) | 75.2 (.23) | 72.9 (.12) |
| Physical | 88.5 | 84.6 (.45) | 80.0 (.23) | 86.9 (.33) | 82.0 (.24) | 87.5 (.42) |
| Emotional | 78.5 | 79.3 (.89) | 67.0 (.24) | 85.5 (.88) | 75.0 (.37) | 84.3 (.79) |
| Social | 87.7 | 75.7 (.09) | 77.0 (.17) | 75.0 (.09) | 81.3 (.21) | 69.3 (.08) |
| School | 78.9 | 67.3 (.08) | 58.0 (.05) | 72.0 (.19) | 69.4 (.15) | 65.0 (.09) |
All mean comparisons were made against UK norms17 using the 1 sample t test.