Table 4

Histiocytoses of the R group

Histiocytoses of the R group
Familial RDD 
 Faisalabad (or H) syndrome (OMIM #602782
 FAS deficiency or ALPS-related RDD (OMIM #601859
 Familial RDD not otherwise specified 
Classical (nodal) RDD 
 Without IgG4 syndrome 
 IgG4 associated 
Extranodal RDD 
 Bone RDD 
 CNS RDD without IgG4 syndrome 
 CNS RDD, IgG4 associated 
 Single-organ RDD other than lymph node, skin, and CNS, without IgG4 syndrome 
 Single-organ RDD other than lymph node, skin, and CNS, IgG4 associated 
 Disseminated RDD 
Neoplasia-associated RDD 
 RDD postleukemia 
 RDD postlymphoma 
 RDD associated with MH 
 RDD associated with LCH or ECD 
Immune disease-associated RDD 
 SLE related 
 IJA related 
 AIHA associated 
 HIV associated 
Other non-C non-L non-M non-H histiocytoses 
Histiocytoses of the R group
Familial RDD 
 Faisalabad (or H) syndrome (OMIM #602782
 FAS deficiency or ALPS-related RDD (OMIM #601859
 Familial RDD not otherwise specified 
Classical (nodal) RDD 
 Without IgG4 syndrome 
 IgG4 associated 
Extranodal RDD 
 Bone RDD 
 CNS RDD without IgG4 syndrome 
 CNS RDD, IgG4 associated 
 Single-organ RDD other than lymph node, skin, and CNS, without IgG4 syndrome 
 Single-organ RDD other than lymph node, skin, and CNS, IgG4 associated 
 Disseminated RDD 
Neoplasia-associated RDD 
 RDD postleukemia 
 RDD postlymphoma 
 RDD associated with MH 
 RDD associated with LCH or ECD 
Immune disease-associated RDD 
 SLE related 
 IJA related 
 AIHA associated 
 HIV associated 
Other non-C non-L non-M non-H histiocytoses 

AIHA, autoimmune hemolytic anemia; IJA, idiopathic juvenile arthritis; OMIM, Online Mendelian Inheritance in Man.

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