Table 2

Scoring systems for the diagnosis of secondary HLH

HScoreDelphi study
Known underlying immunodepression Predisposing underlying disease 
High temperature Fever 
Organomegaly Organomegaly 
Hyperferritinemia Hyperferritinemia 
Cytopenia Cytopenia 
Hemophagocytosis Hemophagocytosis 
Hypertriglyceridemia Elevated LDH 
Hypofibrinogenemia  
Elevated SGOT/ALT  
HScoreDelphi study
Known underlying immunodepression Predisposing underlying disease 
High temperature Fever 
Organomegaly Organomegaly 
Hyperferritinemia Hyperferritinemia 
Cytopenia Cytopenia 
Hemophagocytosis Hemophagocytosis 
Hypertriglyceridemia Elevated LDH 
Hypofibrinogenemia  
Elevated SGOT/ALT  

ALT, alanine aminotransferase; SGOT, serum glutamic oxaloacetic transaminase.

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