Proposed ECD classification
| Clinical severity and organ system dominance . |
|---|
| Asymptomatic or minimally symptomatic ECD |
| Cutaneous-dominant disease |
| Minimal or asymptomatic bone disease |
| Symptomatic ECD |
| CNS dominant |
| Cardiac dominant |
| Retroperitoneal dominant |
| Orbital-craniofacial dominant |
| Neuroendocrine dominant |
| Pulmonary dominant |
| Multisystem |
| Clinical severity and organ system dominance . |
|---|
| Asymptomatic or minimally symptomatic ECD |
| Cutaneous-dominant disease |
| Minimal or asymptomatic bone disease |
| Symptomatic ECD |
| CNS dominant |
| Cardiac dominant |
| Retroperitoneal dominant |
| Orbital-craniofacial dominant |
| Neuroendocrine dominant |
| Pulmonary dominant |
| Multisystem |