Table 1

Causes of neutropenia in adults

Congenital* 
 Constitutional neutropenia 
 Ethnic neutropenia 
 Benign familial neutropenia 
 Cyclic neutropenia 
Acquired 
 Infection-associated 
  Post-infectious 
  Active infection (sepsis, viruses) 
 Drug-induced 
  Agranulocytosis 
  Mild neutropenia 
 Autoimmune 
  Primary autoimmune 
  Secondary autoimmune 
  Felty syndrome 
 Malignancy 
  Acute leukemia 
  Myelodysplasia 
  LGL leukemia 
  Myeloma, lymphoma 
  Myelophthisic processes 
 Dietary 
  B12, folate deficiency 
  Copper deficiency 
  Global caloric malnutrition 
Congenital* 
 Constitutional neutropenia 
 Ethnic neutropenia 
 Benign familial neutropenia 
 Cyclic neutropenia 
Acquired 
 Infection-associated 
  Post-infectious 
  Active infection (sepsis, viruses) 
 Drug-induced 
  Agranulocytosis 
  Mild neutropenia 
 Autoimmune 
  Primary autoimmune 
  Secondary autoimmune 
  Felty syndrome 
 Malignancy 
  Acute leukemia 
  Myelodysplasia 
  LGL leukemia 
  Myeloma, lymphoma 
  Myelophthisic processes 
 Dietary 
  B12, folate deficiency 
  Copper deficiency 
  Global caloric malnutrition 
*

Excludes forms of congenital neutropenia that would be diagnosed in childhood (eg, severe congenital neutropenia or neutropenia occurring in the context of a larger congenital syndrome).

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