Table 1

Summary of laboratory findings in the members of the kindred

I.1II.1II.2II.3
IgG (g/L) 5.53 11.4 2.7 1.64 
IgA (g/L) 0.18 1.86 0.1 
IgM (g/L) 0.09 0.66 0.4 0.05 
Specific antibodies On IVIG  Tetanus toxoid 0.16 IU/mL PNab detected for 7/14 serotypes* On IVIG 
Lymphocytes (×109/L) 2.7 1.8 1.9 2.0 
IgE (kU/L) 175 <2 <2 
CD4 (×109/L) 1.46 NA 0.92 0.74 
CD8 (×109/L) 0.99 BA 0.74 1.75 
B cells (×109/L) 23.1 0.02 
I.1II.1II.2II.3
IgG (g/L) 5.53 11.4 2.7 1.64 
IgA (g/L) 0.18 1.86 0.1 
IgM (g/L) 0.09 0.66 0.4 0.05 
Specific antibodies On IVIG  Tetanus toxoid 0.16 IU/mL PNab detected for 7/14 serotypes* On IVIG 
Lymphocytes (×109/L) 2.7 1.8 1.9 2.0 
IgE (kU/L) 175 <2 <2 
CD4 (×109/L) 1.46 NA 0.92 0.74 
CD8 (×109/L) 0.99 BA 0.74 1.75 
B cells (×109/L) 23.1 0.02 

NA, not applicable; PNab, antibodies to pneumococcal polysaccharides.

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