Table 1 WHO 2008 mature T-cell and... | American Society of Hematology

Table 1

WHO 2008 mature T-cell and NK-cell neoplasms

Mature T-cell and NK-cell neoplasms	Incidence (%)*
T-cell prolymphocytic leukemia
T-cell large granular lymphocytic leukemia
Chronic lymphoproliferative disorder of NK cells†
Aggressive NK-cell leukemia
Systemic EBV-positive T-cell lymphoproliferative disease of childhood
Hydroa vacciniforme-like lymphoma
Adult T-cell leukemia/lymphoma	9.6
Extranodal NK/T-cell lymphoma, nasal type	10.4
Enteropathy-associated T-cell lymphoma	4.7
Hepatosplenic T-cell lymphoma
Subcutaneous panniculitis-like T-cell lymphoma	0.9
Mycosis fungoides
Sézary syndrome
Primary cutaneous CD30⁺ T-cell lymphoproliferative disorders
Lymphomatoid papulosis
Primary cutaneous anaplastic large cell lymphoma	1.7
Primary cutaneous γδ T-cell lymphoma
Primary cutaneous CD8⁺ aggressive epidermotropic cytotoxic T-cell lymphoma†
Primary cutaneous CD4⁺ small/medium T-cell lymphoma†
Peripheral T-cell lymphoma, NOS	25.6
Angioimmunoblastic T-cell lymphoma	19.5
Anaplastic large cell lymphoma, ALK-positive	6.6
Anaplastic large cell lymphoma, ALK-negative†	5.5

Mature T-cell and NK-cell neoplasms	Incidence (%)*
T-cell prolymphocytic leukemia
T-cell large granular lymphocytic leukemia
Chronic lymphoproliferative disorder of NK cells†
Aggressive NK-cell leukemia
Systemic EBV-positive T-cell lymphoproliferative disease of childhood
Hydroa vacciniforme-like lymphoma
Adult T-cell leukemia/lymphoma	9.6
Extranodal NK/T-cell lymphoma, nasal type	10.4
Enteropathy-associated T-cell lymphoma	4.7
Hepatosplenic T-cell lymphoma
Subcutaneous panniculitis-like T-cell lymphoma	0.9
Mycosis fungoides
Sézary syndrome
Primary cutaneous CD30⁺ T-cell lymphoproliferative disorders
Lymphomatoid papulosis
Primary cutaneous anaplastic large cell lymphoma	1.7
Primary cutaneous γδ T-cell lymphoma
Primary cutaneous CD8⁺ aggressive epidermotropic cytotoxic T-cell lymphoma†
Primary cutaneous CD4⁺ small/medium T-cell lymphoma†
Peripheral T-cell lymphoma, NOS	25.6
Angioimmunoblastic T-cell lymphoma	19.5
Anaplastic large cell lymphoma, ALK-positive	6.6
Anaplastic large cell lymphoma, ALK-negative†	5.5

Incidence among peripheral T-cell and NK/T-cell lymphoma from the International T-Cell Project.

Provisional entities.