Table 1

Diseases that can demonstrate iMCD-like histopathology and diseases reported to cooccur with iMCD

NeoplasticInflammatoryInfectious/toxin ingestion
iMCD-like histopathology   
 Non-Hodgkin lymphoma Systemic lupus erythematous Epstein-Barr virus 
 Cutaneous lymphoma Rheumatoid arthritis HIV 
 Hodgkin lymphoma Sjogren syndrome Hydrochoride ingestion 
 Cardiac myxoma Relapsing polychondritis  
 Multiple myeloma Systemic IGG4 plasmacytic syndrome  
 Clear cell meningioma Systemic/cutaneous plasmacytosis  
 Choroid meningioma   
 Giant cell carcinoma of lung   
 Calcifying fibrous pseudotumor   
 Inflammatory myofibroblastic tumor   
Cooccur with iMCD   
 POEMS syndrome Adult onset Still’s disease Human herpes virus 6 
 Paraneoplastic pemphigus Systemic juvenile idiopathic arthritis Hepatitis b virus 
 Melanoma Sarcoidosis Toxoplasma 
 Angioimmunoblastic T-cell lymphoma Amyloidosis Mycobacterium tuberculosis 
 Indolent T-lymphoblastic proliferation Pure red cell aplasia Cytomegalovirus 
 Inflammatory hepatocellular adenoma Acquired factor VIII deficiency Toxoplasma 
 Myasthenia gravis  
 Familial mediterranean fever  
 Glomerulonephritides  
NeoplasticInflammatoryInfectious/toxin ingestion
iMCD-like histopathology   
 Non-Hodgkin lymphoma Systemic lupus erythematous Epstein-Barr virus 
 Cutaneous lymphoma Rheumatoid arthritis HIV 
 Hodgkin lymphoma Sjogren syndrome Hydrochoride ingestion 
 Cardiac myxoma Relapsing polychondritis  
 Multiple myeloma Systemic IGG4 plasmacytic syndrome  
 Clear cell meningioma Systemic/cutaneous plasmacytosis  
 Choroid meningioma   
 Giant cell carcinoma of lung   
 Calcifying fibrous pseudotumor   
 Inflammatory myofibroblastic tumor   
Cooccur with iMCD   
 POEMS syndrome Adult onset Still’s disease Human herpes virus 6 
 Paraneoplastic pemphigus Systemic juvenile idiopathic arthritis Hepatitis b virus 
 Melanoma Sarcoidosis Toxoplasma 
 Angioimmunoblastic T-cell lymphoma Amyloidosis Mycobacterium tuberculosis 
 Indolent T-lymphoblastic proliferation Pure red cell aplasia Cytomegalovirus 
 Inflammatory hepatocellular adenoma Acquired factor VIII deficiency Toxoplasma 
 Myasthenia gravis  
 Familial mediterranean fever  
 Glomerulonephritides  

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