Table 1

Characteristics of the patients in the analysis

N = 111 patients
Age, median (range) 66 (40-84) 
Males/females (%) 60/40 
Organ involvement (%)  
 Cardiac 65 
 Renal 71 
 Liver 15 
 PNS 19 
 Soft tissue 21 
Number of involved organs, (range) 2 (1-4) 
NT-proBNP (pg/mL), median (range) 2297 (17.0-121 000) 
hsTnT (ng/L), median (range) 42 (3-338) 
Involved FLC (mg/L), median (range) 235 (9-900) 
Mayo stage (%)  
 I 20 
 II 49 
 III 31 
Stage IIIB (Mayo stage III and NTproBNP >8500 pg/mL) (%) 19 
Proteinuria g/day, median (range) 4.8 (0.5-39) 
eGFR mL/min/1.73 m2, median (range) 71 (8 to >150) 
VWF U/dL, median (range) 203.0 (20.0-1046.0) 
IQR (range) 127.0-235.0 
ADAMTS-13 ng/mL, median (range) 1044 (770-1600) 
N = 111 patients
Age, median (range) 66 (40-84) 
Males/females (%) 60/40 
Organ involvement (%)  
 Cardiac 65 
 Renal 71 
 Liver 15 
 PNS 19 
 Soft tissue 21 
Number of involved organs, (range) 2 (1-4) 
NT-proBNP (pg/mL), median (range) 2297 (17.0-121 000) 
hsTnT (ng/L), median (range) 42 (3-338) 
Involved FLC (mg/L), median (range) 235 (9-900) 
Mayo stage (%)  
 I 20 
 II 49 
 III 31 
Stage IIIB (Mayo stage III and NTproBNP >8500 pg/mL) (%) 19 
Proteinuria g/day, median (range) 4.8 (0.5-39) 
eGFR mL/min/1.73 m2, median (range) 71 (8 to >150) 
VWF U/dL, median (range) 203.0 (20.0-1046.0) 
IQR (range) 127.0-235.0 
ADAMTS-13 ng/mL, median (range) 1044 (770-1600) 

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