Table 2

Selected complications

Associated conditionNo.% of cohort (n = 473)
Infections only (no complications) 151 31.9 
Chronic lung disease (functional/structural) 135 28.5 
Bronchiectasis 53 11.2 
Autoimmunity 134 28.6 
    ITP 67 14.2 
    AIHA 33 
    Evans syndrome 20 4.2 
    Rheumatoid arthritis 15 3.2 
    Anti-IgA antibody 1.5 
    Alopecia 1.1 
    Neutropenia, pernicious anemia, anticardiolipin antibody, antiphospholipid syndrome, diabetes mellitus, juvenile rheumatoid arthritis, uveitis, multiple sclerosis, systemic lupus erythematosis, autoimmune thyroid disease, lichen planus, vasculitis, vitiligo, psoriasis < 5 < 1 
Gastrointestinal disease 73 15.4 
    Malabsorption 28 5.9 
    Inflammatory bowel disease (Crohn disease, ulcerative colitis, ulcerative proctitis) 20 4.2 
    Chronic diarrhea 1.9 
    Idiopathic mucosal inflammation 1.3 
    Nodular lymphoid hyperplasia 1.1 
    Gastrointestinal bleeding, irritable bowel syndrome, partial gastrectomy, diverticulitis, esophagitis < 1 
Liver disease/hepatitis 43 9.1 
    Hepatitis C 1.9 
    Liver granuloma 1.7 
    Idiopathic liver disease 1.7 
    Non-A, non-B hepatitis* 1.3 
    Chronic hepatitis of unknown origin 1.1 
    Primary biliary cirrhosis < 1 
    Nodular regenerative hyperplasia < 1 
    Hepatitis B, cirrhosis of unknown etiology < 1 
Associated conditionNo.% of cohort (n = 473)
Infections only (no complications) 151 31.9 
Chronic lung disease (functional/structural) 135 28.5 
Bronchiectasis 53 11.2 
Autoimmunity 134 28.6 
    ITP 67 14.2 
    AIHA 33 
    Evans syndrome 20 4.2 
    Rheumatoid arthritis 15 3.2 
    Anti-IgA antibody 1.5 
    Alopecia 1.1 
    Neutropenia, pernicious anemia, anticardiolipin antibody, antiphospholipid syndrome, diabetes mellitus, juvenile rheumatoid arthritis, uveitis, multiple sclerosis, systemic lupus erythematosis, autoimmune thyroid disease, lichen planus, vasculitis, vitiligo, psoriasis < 5 < 1 
Gastrointestinal disease 73 15.4 
    Malabsorption 28 5.9 
    Inflammatory bowel disease (Crohn disease, ulcerative colitis, ulcerative proctitis) 20 4.2 
    Chronic diarrhea 1.9 
    Idiopathic mucosal inflammation 1.3 
    Nodular lymphoid hyperplasia 1.1 
    Gastrointestinal bleeding, irritable bowel syndrome, partial gastrectomy, diverticulitis, esophagitis < 1 
Liver disease/hepatitis 43 9.1 
    Hepatitis C 1.9 
    Liver granuloma 1.7 
    Idiopathic liver disease 1.7 
    Non-A, non-B hepatitis* 1.3 
    Chronic hepatitis of unknown origin 1.1 
    Primary biliary cirrhosis < 1 
    Nodular regenerative hyperplasia < 1 
    Hepatitis B, cirrhosis of unknown etiology < 1 
*

Diagnosed before availability of the hepatitis C PCR.

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