Table 1

Classification of pulmonary hypertension according to the World Symposium on Pulmonary Hypertension

GroupDefinition
Pulmonary arterial hypertension 
Pulmonary hypertension due to left heart disease 
Pulmonary hypertension due to lung diseases and/or hypoxia 
CTEPH 
Pulmonary hypertension with unclear or multifactorial mechanisms 
GroupDefinition
Pulmonary arterial hypertension 
Pulmonary hypertension due to left heart disease 
Pulmonary hypertension due to lung diseases and/or hypoxia 
CTEPH 
Pulmonary hypertension with unclear or multifactorial mechanisms 
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