Table 1

Baseline demographics and treatment received

Value
Baseline demographics  
    Age, y  
        Median 30 
        Range 1-94 
    Sex, %  
        Male 38 
        Female 62 
Prior treatments received, no. (%)  
    Steroid 406 (52) 
    IVIG 399 (52) 
    Intravenous anti-D 277 (36) 
    Steroids and IVIG 292 (38) 
    Steroids and intravenous anti-D 201 (26) 
    Steroids, IVIG, and intravenous anti-D 161 (21) 
Ig levels, mg/dL  
    IgA median 166 
    IgA range 6.6-1535 
    IgM median 114 
    IgM range 7-1550 
    IgG median 1120 
    IgG range 128-6710 
Subjects with abnormal Ig  
    Elevated IgA, no. (%) 107 (14) 
    Low IgA, no. (%) 114 (15) 
    Elevated IgM, no. (%) 29 (4) 
    Low IgM, no. (%) 85 (11) 
    Elevated IgG, no. (%) 245 (32) 
    Low IgG, no. (%) 66 (9) 
Value
Baseline demographics  
    Age, y  
        Median 30 
        Range 1-94 
    Sex, %  
        Male 38 
        Female 62 
Prior treatments received, no. (%)  
    Steroid 406 (52) 
    IVIG 399 (52) 
    Intravenous anti-D 277 (36) 
    Steroids and IVIG 292 (38) 
    Steroids and intravenous anti-D 201 (26) 
    Steroids, IVIG, and intravenous anti-D 161 (21) 
Ig levels, mg/dL  
    IgA median 166 
    IgA range 6.6-1535 
    IgM median 114 
    IgM range 7-1550 
    IgG median 1120 
    IgG range 128-6710 
Subjects with abnormal Ig  
    Elevated IgA, no. (%) 107 (14) 
    Low IgA, no. (%) 114 (15) 
    Elevated IgM, no. (%) 29 (4) 
    Low IgM, no. (%) 85 (11) 
    Elevated IgG, no. (%) 245 (32) 
    Low IgG, no. (%) 66 (9) 
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