Table 1

Primary hematologic diagnoses transfusion burden of study population

DiagnosisN (% of total)Mean transfusion burden, mg iron/kg per d (mean ± SD)
β-thalassemia major 38 (75) 0.389 ± 0.106 
α-thalassemia major 2 (4) 0.278 ± 0.055* 
Non-thalassemia major disorders 11 (21) 0.283 ± 0.083 
    β-thalassemia intermedia (transfused > 7/year) 2 (4) 0.203 ± 0.024* 
    HbE-β0 thalassemia 6 (12) 0.304 ± 0.098 
    Sickle cell disease 3 (6) 0.293 ± 0.077 
DiagnosisN (% of total)Mean transfusion burden, mg iron/kg per d (mean ± SD)
β-thalassemia major 38 (75) 0.389 ± 0.106 
α-thalassemia major 2 (4) 0.278 ± 0.055* 
Non-thalassemia major disorders 11 (21) 0.283 ± 0.083 
    β-thalassemia intermedia (transfused > 7/year) 2 (4) 0.203 ± 0.024* 
    HbE-β0 thalassemia 6 (12) 0.304 ± 0.098 
    Sickle cell disease 3 (6) 0.293 ± 0.077 
*

Plus or minus range for N = 2.

Significantly different from β-thalassemia major (P = .0036 by unpaired t test).

Receiving at least 7 transfusions annually before and during study period.

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