Primary hematologic diagnoses transfusion burden of study population
Diagnosis . | N (% of total) . | Mean transfusion burden, mg iron/kg per d (mean ± SD) . |
---|---|---|
β-thalassemia major | 38 (75) | 0.389 ± 0.106 |
α-thalassemia major | 2 (4) | 0.278 ± 0.055* |
Non-thalassemia major disorders | 11 (21) | 0.283 ± 0.083† |
β-thalassemia intermedia‡ (transfused > 7/year) | 2 (4) | 0.203 ± 0.024* |
HbE-β0 thalassemia | 6 (12) | 0.304 ± 0.098 |
Sickle cell disease | 3 (6) | 0.293 ± 0.077 |
Diagnosis . | N (% of total) . | Mean transfusion burden, mg iron/kg per d (mean ± SD) . |
---|---|---|
β-thalassemia major | 38 (75) | 0.389 ± 0.106 |
α-thalassemia major | 2 (4) | 0.278 ± 0.055* |
Non-thalassemia major disorders | 11 (21) | 0.283 ± 0.083† |
β-thalassemia intermedia‡ (transfused > 7/year) | 2 (4) | 0.203 ± 0.024* |
HbE-β0 thalassemia | 6 (12) | 0.304 ± 0.098 |
Sickle cell disease | 3 (6) | 0.293 ± 0.077 |