Table 2

Symptoms of chronic active EBV

PatientFeverLymphadenopathySplenomegalyHepatomegalyCNS diseasePeripheral neuropathyInterstitial pneumonitisPancytopeniaHepatitisHemophagocytosisHypogammaglobulinemiaOther
Unknown whether B-, T-, or NK-cell disease             
    1      
    2        
    4           
    5        Autoimmune hemolytic anemia, sinusitis 
B-cell disease             
    3        Autoimmune hemolytic anemia, neutropenia, skin disease, vasculitis, sinusitis, thrombocytopenia 
    6    Uveitis 
    7         Sinusitis, vasculitis 
    8          
    9    
    11      Autoimmune hemolytic anemia 
    12      Eye disease, skin disease 
    13       Skin disease 
    14          
    16          
    17        Sinusitis 
T-cell disease             
    10     Sinusitis, thrombocytopenia 
    15         Hydroa vacciniforme 
    18       Conjunctivitis 
NK-cell disease             
    19            Skin disease, mosquito bite hypersensitivity 
PatientFeverLymphadenopathySplenomegalyHepatomegalyCNS diseasePeripheral neuropathyInterstitial pneumonitisPancytopeniaHepatitisHemophagocytosisHypogammaglobulinemiaOther
Unknown whether B-, T-, or NK-cell disease             
    1      
    2        
    4           
    5        Autoimmune hemolytic anemia, sinusitis 
B-cell disease             
    3        Autoimmune hemolytic anemia, neutropenia, skin disease, vasculitis, sinusitis, thrombocytopenia 
    6    Uveitis 
    7         Sinusitis, vasculitis 
    8          
    9    
    11      Autoimmune hemolytic anemia 
    12      Eye disease, skin disease 
    13       Skin disease 
    14          
    16          
    17        Sinusitis 
T-cell disease             
    10     Sinusitis, thrombocytopenia 
    15         Hydroa vacciniforme 
    18       Conjunctivitis 
NK-cell disease             
    19            Skin disease, mosquito bite hypersensitivity