Table 2

Diseases associated with T-LGL leukemia

Associated diseasesFrequency, %
Autoimmune diseases 15-40 
    RA 11-36 
    Sjogren syndrome CR 
    Polymyositis CR 
    PMR CR 
    Multineuritis CR 
    Vasculitis CR 
    Endocrinopathy CR 
    Celiac disease CR 
    CIBD CR 
    APECED CR 
Autoimmune cytopenia* 5-10 
    PRCA 
    AIHA < 2 
    ITP Rare 
Cyclic neutropenia Rare 
Pulmonary hypertension Rare 
Neoplasia < 10 
    Solid tumors < 4 
    Myelodysplasia < 4 
    B-cell malignancies 5-7 
    CML treated with dasatinib Recently described 
Viral infection (HIV, CMV, HCV, EBV) Rare 
Posttransplantation  
    Solid and hematopoietic stem cell transplantation Rare 
Associated diseasesFrequency, %
Autoimmune diseases 15-40 
    RA 11-36 
    Sjogren syndrome CR 
    Polymyositis CR 
    PMR CR 
    Multineuritis CR 
    Vasculitis CR 
    Endocrinopathy CR 
    Celiac disease CR 
    CIBD CR 
    APECED CR 
Autoimmune cytopenia* 5-10 
    PRCA 
    AIHA < 2 
    ITP Rare 
Cyclic neutropenia Rare 
Pulmonary hypertension Rare 
Neoplasia < 10 
    Solid tumors < 4 
    Myelodysplasia < 4 
    B-cell malignancies 5-7 
    CML treated with dasatinib Recently described 
Viral infection (HIV, CMV, HCV, EBV) Rare 
Posttransplantation  
    Solid and hematopoietic stem cell transplantation Rare 

PMR indicates polymyalgia rheumatica; CIBD, chronic inflammatory bowel disease; APECED, autoimmune polyendocrinopathy-candidosis-ectodermal dystrophy; PRCA, pure red cell aplasia; AIHA, autoimmune hemolytic anemia; ITP, idiopathic thrombocytopenic purpura; CML, chronic myeloid leukemia; CMV, cytomegalovirus; HCV, hepatitis C virus; EBV, Epstein-Barr virus; and CR, case report.

*

Excluding chronic neutropenia.

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