Diseases associated with T-LGL leukemia
Associated diseases . | Frequency, % . |
---|---|
Autoimmune diseases | 15-40 |
RA | 11-36 |
Sjogren syndrome | CR |
Polymyositis | CR |
PMR | CR |
Multineuritis | CR |
Vasculitis | CR |
Endocrinopathy | CR |
Celiac disease | CR |
CIBD | CR |
APECED | CR |
Autoimmune cytopenia* | 5-10 |
PRCA | 5 |
AIHA | < 2 |
ITP | Rare |
Cyclic neutropenia | Rare |
Pulmonary hypertension | Rare |
Neoplasia | < 10 |
Solid tumors | < 4 |
Myelodysplasia | < 4 |
B-cell malignancies | 5-7 |
CML treated with dasatinib | Recently described |
Viral infection (HIV, CMV, HCV, EBV) | Rare |
Posttransplantation | |
Solid and hematopoietic stem cell transplantation | Rare |
Associated diseases . | Frequency, % . |
---|---|
Autoimmune diseases | 15-40 |
RA | 11-36 |
Sjogren syndrome | CR |
Polymyositis | CR |
PMR | CR |
Multineuritis | CR |
Vasculitis | CR |
Endocrinopathy | CR |
Celiac disease | CR |
CIBD | CR |
APECED | CR |
Autoimmune cytopenia* | 5-10 |
PRCA | 5 |
AIHA | < 2 |
ITP | Rare |
Cyclic neutropenia | Rare |
Pulmonary hypertension | Rare |
Neoplasia | < 10 |
Solid tumors | < 4 |
Myelodysplasia | < 4 |
B-cell malignancies | 5-7 |
CML treated with dasatinib | Recently described |
Viral infection (HIV, CMV, HCV, EBV) | Rare |
Posttransplantation | |
Solid and hematopoietic stem cell transplantation | Rare |
PMR indicates polymyalgia rheumatica; CIBD, chronic inflammatory bowel disease; APECED, autoimmune polyendocrinopathy-candidosis-ectodermal dystrophy; PRCA, pure red cell aplasia; AIHA, autoimmune hemolytic anemia; ITP, idiopathic thrombocytopenic purpura; CML, chronic myeloid leukemia; CMV, cytomegalovirus; HCV, hepatitis C virus; EBV, Epstein-Barr virus; and CR, case report.
Excluding chronic neutropenia.