Table 1

World Health Organization classification of myeloid malignancies and operational subcategorization of myeloproliferative neoplasms

  1. Acute myeloid leukemia and related precursor neoplasms

  2. Myelodysplastic syndromes (MDS)

  3. Myeloproliferative neoplasms (MPN)

    • Classic MPN

      • Chronic myelogenous leukemia (CML), BCR-ABL1 positive

      • Polycythemia vera (PV)

        1. Chronic phase PV

        2. Post-PV MF

        3. Blast phase PV

      • Essential thrombocythemia (ET)

        1. Chronic phase ET

        2. Post-ET MF

        3. Blast phase ET

      • Primary myelofibrosis (PMF)

        1. Chronic phase PMF

        2. Blast phase PMF

    • Non-classic MPN

      • Chronic neutrophilic leukemia

      • Chronic eosinophilic leukemia, not otherwise specified

      • Mastocytosis

      • Myeloproliferative neoplasm, unclassifiable (MPN-U)

  4. MDS/MPN

  5. Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA,* PDGFRB,* or FGFR1*

 
  1. Acute myeloid leukemia and related precursor neoplasms

  2. Myelodysplastic syndromes (MDS)

  3. Myeloproliferative neoplasms (MPN)

    • Classic MPN

      • Chronic myelogenous leukemia (CML), BCR-ABL1 positive

      • Polycythemia vera (PV)

        1. Chronic phase PV

        2. Post-PV MF

        3. Blast phase PV

      • Essential thrombocythemia (ET)

        1. Chronic phase ET

        2. Post-ET MF

        3. Blast phase ET

      • Primary myelofibrosis (PMF)

        1. Chronic phase PMF

        2. Blast phase PMF

    • Non-classic MPN

      • Chronic neutrophilic leukemia

      • Chronic eosinophilic leukemia, not otherwise specified

      • Mastocytosis

      • Myeloproliferative neoplasm, unclassifiable (MPN-U)

  4. MDS/MPN

  5. Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA,* PDGFRB,* or FGFR1*

 
*

Genetic rearrangements involving platelet-derived growth factor receptor α/β (PDGFRA/PDGFRB) or fibroblast growth factor receptor 1 (FGFR1).

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