Table 2

Clinical predictors of poor survival in ECD (multivariate survival analysis using the Cox proportional hazard model)

VariableUnivariate analysis (P)Cox multivariate survival analysis*
HR (95% CI)P
Sex .55   
Cardiovascular involvement .57   
CNS involvement .10 2.43 (1.33-4.94) .004 
Hypophyseal involvement .93   
Paranasal sinus involvement .54   
Maxillary involvement .23   
Xanthelasma .98   
Orbital involvement .57   
Pulmonary involvement .21   
Retroperitoneal involvement .31   
Adrenal involvement .53   
VariableUnivariate analysis (P)Cox multivariate survival analysis*
HR (95% CI)P
Sex .55   
Cardiovascular involvement .57   
CNS involvement .10 2.43 (1.33-4.94) .004 
Hypophyseal involvement .93   
Paranasal sinus involvement .54   
Maxillary involvement .23   
Xanthelasma .98   
Orbital involvement .57   
Pulmonary involvement .21   
Retroperitoneal involvement .31   
Adrenal involvement .53   

P < .20 in univariate analysis were entered in the multivariate model.

*

Adjusted for the age at compilation (quartiles of the distribution).

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