Table 1

Patient series

Case no.SexAge, yDiagnosisCutaneous involvementExtracutaneous lesionsTreatmentOutcome, mo
55 PC-ENK/T-NT Nodules arms, abdomen Pharynx, pancreas; onset 7 mo after cutaneous lesions Chemotherapy (CHOP) 10* 
74 PC-ENK/T-NT Nodules and ulcerations right leg, abdomen None Chemotherapy (CHOP) 24* 
67 ENK/T-N Multiple nodules and ulcerations face, arms, abdomen, legs, genital Nasal and paranasal cavities; onset simultaneous with cutaneous lesions Chemotherapy (CHOP) + radiotherapy 15* 
43 PC-ENK/T-NT Nodules arms None Chemotherapy (CHOP) + ganciclovir-butyrate 12* 
61 PC-ENK/T-NT Nodules left arm Lymphadenopathy left axilla; onset 3 mo after cutaneous lesions Chemotherapy (CHOP) 4* 
Case no.SexAge, yDiagnosisCutaneous involvementExtracutaneous lesionsTreatmentOutcome, mo
55 PC-ENK/T-NT Nodules arms, abdomen Pharynx, pancreas; onset 7 mo after cutaneous lesions Chemotherapy (CHOP) 10* 
74 PC-ENK/T-NT Nodules and ulcerations right leg, abdomen None Chemotherapy (CHOP) 24* 
67 ENK/T-N Multiple nodules and ulcerations face, arms, abdomen, legs, genital Nasal and paranasal cavities; onset simultaneous with cutaneous lesions Chemotherapy (CHOP) + radiotherapy 15* 
43 PC-ENK/T-NT Nodules arms None Chemotherapy (CHOP) + ganciclovir-butyrate 12* 
61 PC-ENK/T-NT Nodules left arm Lymphadenopathy left axilla; onset 3 mo after cutaneous lesions Chemotherapy (CHOP) 4* 

PC-ENK/T-NT indicates primary cutaneous extranodal natural killer/T-cell lymphoma nasal-type; CHOP, cyclophosphamide, doxorubicin, vincristine, prednisone; ENK/T-N, extranodal natural killer/T-cell lymphoma nasal.

*

Death.

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