Characteristics and treatment of patients included in the present series
Patient no. . | Diagnosis . | Age, y . | Sex . | MIg . | Gammopathy . | Atherosclerosis . | Treatment . |
---|---|---|---|---|---|---|---|
1 | NXG | 67 | Female | IgG1κ | Stage I MM | No* | Thalidomide (no improvement) |
2 | NXG | 65 | Female | IgGκ | Stage I MM | No | Steroids/immunosuppressive therapy (no improvement) |
3 | NXG | 63 | Male | IgGλ | MGUS/myelodysplasia | Yes, ischemic cardiopathy | Thalidomide/bortezomib (improvement), PR |
4 | NXG | 71 | Female | IgGλ | MGUS | Yes, aortic aneurysm | Steroids/chlorambucil† (improvement), PR |
5 | NXG | 72 | Female | IgGκ | MGUS | Yes, hypertensive cardiopathy | Steroids/chlorambucil† (improvement), PR |
6 | NXG | 48 | Male | IgG1κ | Lymphoma | No | Chlorambucil/rituximab/fludarabine/cyclophosphamide (improvement), VGPR |
7 | NXG | 53 | Male | IgG1κ | MGUS | No | Chlorambucil†/rituximab†/fludarabine†/cyclophosphamide/thalidomide/dexamethasone (improvement), VGPR |
8 | NXG | 65 | Female | IgGκ | Overt MM | No | Melphalan/prednisone/interferon-α (improvement), VGPR |
9 | NXG | 78 | Female | IgGκ IgMλ | MGUS | No | None |
10 | NXG | 65 | Female | IgGλ | Overt MM | No | None |
11 | NXG | 68 | Female | IgGκ | MGUS | No | None |
12 | NX | 72 | Female | IgGκ | MGUS | No | None |
13 | NX | 37 | Female | IgGκ | Stage I MM | No* | High-dose therapy and autotransplant (no improvement) |
14 | NX | 75 | Male | IgG1λ | Overt MM | No* | Melphalan/prednisone (no improvement) |
15 | NX | 60 | Male | IgGκ IgMκ | Waldenström/amyloidosis | No | Chlorambucil |
16 | NX | 68 | Male | IgG1κ | MGUS | Yes, ischemic cardiopathy, severe arteritis | None |
17 | NX | 66 | Male | IgGλ | MGUS | No* | None |
18 | NX | 52 | Male | IgGλ | MGUS | No* | None |
19 | NX | 46 | Male | IgGλ | MGUS | No | None |
20 | NX | 42 | Male | IgGλ | MGUS | No | None |
21 | NX | 63 | Male | IgGλ | MGUS | No | None |
22 | NX | 45 | Male | IgGκ | MGUS | No | None |
23 | HX | 74 | Female | IgG1κ | Overt MM | Yes, ischemic cardiopathy | Bortezomib/thalidomide/dexamethasone (complete hematologic and cutaneous response) |
24 | HX | 55 | Male | IgG1κ | Overt MM | Yes, ischemic cardiopathy | Thalidomide/high-dose therapy and autotransplant (improvement), VGPR |
IgG1κ |
Patient no. . | Diagnosis . | Age, y . | Sex . | MIg . | Gammopathy . | Atherosclerosis . | Treatment . |
---|---|---|---|---|---|---|---|
1 | NXG | 67 | Female | IgG1κ | Stage I MM | No* | Thalidomide (no improvement) |
2 | NXG | 65 | Female | IgGκ | Stage I MM | No | Steroids/immunosuppressive therapy (no improvement) |
3 | NXG | 63 | Male | IgGλ | MGUS/myelodysplasia | Yes, ischemic cardiopathy | Thalidomide/bortezomib (improvement), PR |
4 | NXG | 71 | Female | IgGλ | MGUS | Yes, aortic aneurysm | Steroids/chlorambucil† (improvement), PR |
5 | NXG | 72 | Female | IgGκ | MGUS | Yes, hypertensive cardiopathy | Steroids/chlorambucil† (improvement), PR |
6 | NXG | 48 | Male | IgG1κ | Lymphoma | No | Chlorambucil/rituximab/fludarabine/cyclophosphamide (improvement), VGPR |
7 | NXG | 53 | Male | IgG1κ | MGUS | No | Chlorambucil†/rituximab†/fludarabine†/cyclophosphamide/thalidomide/dexamethasone (improvement), VGPR |
8 | NXG | 65 | Female | IgGκ | Overt MM | No | Melphalan/prednisone/interferon-α (improvement), VGPR |
9 | NXG | 78 | Female | IgGκ IgMλ | MGUS | No | None |
10 | NXG | 65 | Female | IgGλ | Overt MM | No | None |
11 | NXG | 68 | Female | IgGκ | MGUS | No | None |
12 | NX | 72 | Female | IgGκ | MGUS | No | None |
13 | NX | 37 | Female | IgGκ | Stage I MM | No* | High-dose therapy and autotransplant (no improvement) |
14 | NX | 75 | Male | IgG1λ | Overt MM | No* | Melphalan/prednisone (no improvement) |
15 | NX | 60 | Male | IgGκ IgMκ | Waldenström/amyloidosis | No | Chlorambucil |
16 | NX | 68 | Male | IgG1κ | MGUS | Yes, ischemic cardiopathy, severe arteritis | None |
17 | NX | 66 | Male | IgGλ | MGUS | No* | None |
18 | NX | 52 | Male | IgGλ | MGUS | No* | None |
19 | NX | 46 | Male | IgGλ | MGUS | No | None |
20 | NX | 42 | Male | IgGλ | MGUS | No | None |
21 | NX | 63 | Male | IgGλ | MGUS | No | None |
22 | NX | 45 | Male | IgGκ | MGUS | No | None |
23 | HX | 74 | Female | IgG1κ | Overt MM | Yes, ischemic cardiopathy | Bortezomib/thalidomide/dexamethasone (complete hematologic and cutaneous response) |
24 | HX | 55 | Male | IgG1κ | Overt MM | Yes, ischemic cardiopathy | Thalidomide/high-dose therapy and autotransplant (improvement), VGPR |
IgG1κ |