Table 1

WAS scoring system according to Zhu et al26  with subsequent refinements27 

Clinical scoresXLT
WAS
0.512345A5M
Thrombocytopenia +/− 
Eczema − − +/− ++ ++/− ++/− 
Immunodeficiency − − +/− ++ ++/− ++/− 
Autoimmunity − − − − − − 
Malignancy − − − − − − 
Clinical scoresXLT
WAS
0.512345A5M
Thrombocytopenia +/− 
Eczema − − +/− ++ ++/− ++/− 
Immunodeficiency − − +/− ++ ++/− ++/− 
Autoimmunity − − − − − − 
Malignancy − − − − − − 

Adapted from Imai27  with permission.

+ indicates present-mild; −, absent; +/−, present-mild or absent; ++, present-severe; and ++/−, present-severe or absent.

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