Table 4

Clinical events more than 2 years after HSCT

Clinical eventsNo. of patients (%)
Overall 43 (48) 
Persistent cGVHD 10 (11) 
Autoimmune/inflammatory events 12 (13) 
    AIHA 
    Myositis 
    Psoriasis, vitiligo, alopecia 
    Ill-defined inflammatory disease 
    Disseminated granulomatous disease 
Severe or recurrent infection 11 (12) 
    Opportunistic infection 
    Recurrent LRTI 
    Chronic sinusitis and/or chronic bronchopneumopathy 
    Viral encephalitis 
Chronic HPV infection 23 (25) 
    Severe HPV infection 
    Mild HPV infection 14 
Nutritional support 18 (20) 
    Enteral feeding 11 
    Parenteral nutrition 
Boost 11 (12) 
Growth insufficiency (weight and/or height less than the third percentile) 16 (18) 
Obesity 3 (3) 
Psychosocial disabilities 6 (7) 
Myelodysplasia* 2 (2) 
Late-onset mortality 8 (9) 
Clinical eventsNo. of patients (%)
Overall 43 (48) 
Persistent cGVHD 10 (11) 
Autoimmune/inflammatory events 12 (13) 
    AIHA 
    Myositis 
    Psoriasis, vitiligo, alopecia 
    Ill-defined inflammatory disease 
    Disseminated granulomatous disease 
Severe or recurrent infection 11 (12) 
    Opportunistic infection 
    Recurrent LRTI 
    Chronic sinusitis and/or chronic bronchopneumopathy 
    Viral encephalitis 
Chronic HPV infection 23 (25) 
    Severe HPV infection 
    Mild HPV infection 14 
Nutritional support 18 (20) 
    Enteral feeding 11 
    Parenteral nutrition 
Boost 11 (12) 
Growth insufficiency (weight and/or height less than the third percentile) 16 (18) 
Obesity 3 (3) 
Psychosocial disabilities 6 (7) 
Myelodysplasia* 2 (2) 
Late-onset mortality 8 (9) 

AIHA indicates autoimmune hemolytic anaemia; and LRTI, lower respiratory tract infection.

*

Patients with reticular dysgenesis.

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