Table 2

IAP genotype and ADAMTS13 activity levels

StrainNo. testedIAP genotypeADAMTS13 activity, mean ± SD, U/mL
FVB/NJ 23 −/− 2.95 ± 0.51 
129x1/SvJ −/− 3.13 ± 0.42 
CAST/EiJ −/− 3.37 ± 0.65 
C57BL/6J 21 +/+ 0.26 ± 0.09 
DBA/2J +/+ 0.24 ± 0.06 
BALB/c +/+ 0.30 ± 0.12 
F1* 10 +/− 2.43 ± 0.43 
F2* 11 −/− 2.51 ± 0.68 
F2* 21 +/− 2.15 ± 0.50 
F2* +/+ 0.30 ± 0.13 
StrainNo. testedIAP genotypeADAMTS13 activity, mean ± SD, U/mL
FVB/NJ 23 −/− 2.95 ± 0.51 
129x1/SvJ −/− 3.13 ± 0.42 
CAST/EiJ −/− 3.37 ± 0.65 
C57BL/6J 21 +/+ 0.26 ± 0.09 
DBA/2J +/+ 0.24 ± 0.06 
BALB/c +/+ 0.30 ± 0.12 
F1* 10 +/− 2.43 ± 0.43 
F2* 11 −/− 2.51 ± 0.68 
F2* 21 +/− 2.15 ± 0.50 
F2* +/+ 0.30 ± 0.13 

All ADAMTS13 activity levels were measured against VWF multimers.

*

F1 = FVB/NJ × C57BL/6J; F2 = F1 × F1.

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