IAP genotype and ADAMTS13 activity levels
Strain . | No. tested . | IAP genotype . | ADAMTS13 activity, mean ± SD, U/mL . |
---|---|---|---|
FVB/NJ | 23 | −/− | 2.95 ± 0.51 |
129x1/SvJ | 6 | −/− | 3.13 ± 0.42 |
CAST/EiJ | 5 | −/− | 3.37 ± 0.65 |
C57BL/6J | 21 | +/+ | 0.26 ± 0.09 |
DBA/2J | 6 | +/+ | 0.24 ± 0.06 |
BALB/c | 6 | +/+ | 0.30 ± 0.12 |
F1* | 10 | +/− | 2.43 ± 0.43 |
F2* | 11 | −/− | 2.51 ± 0.68 |
F2* | 21 | +/− | 2.15 ± 0.50 |
F2* | 4 | +/+ | 0.30 ± 0.13 |
Strain . | No. tested . | IAP genotype . | ADAMTS13 activity, mean ± SD, U/mL . |
---|---|---|---|
FVB/NJ | 23 | −/− | 2.95 ± 0.51 |
129x1/SvJ | 6 | −/− | 3.13 ± 0.42 |
CAST/EiJ | 5 | −/− | 3.37 ± 0.65 |
C57BL/6J | 21 | +/+ | 0.26 ± 0.09 |
DBA/2J | 6 | +/+ | 0.24 ± 0.06 |
BALB/c | 6 | +/+ | 0.30 ± 0.12 |
F1* | 10 | +/− | 2.43 ± 0.43 |
F2* | 11 | −/− | 2.51 ± 0.68 |
F2* | 21 | +/− | 2.15 ± 0.50 |
F2* | 4 | +/+ | 0.30 ± 0.13 |
All ADAMTS13 activity levels were measured against VWF multimers.
F1 = FVB/NJ × C57BL/6J; F2 = F1 × F1.