Hemostatic parameters characterizing the patients
. | Patient 1 . | Patient 2 . | Controls . |
|---|---|---|---|
| Platelet count, × 109/L | < 20 | < 20 | 150-400 |
| Platelet volume, μm3 | 8.5 | 8.5 | 6-8 |
| Platelet agglutinates | + | + | No |
| VWF Ag, % | 75-100 | 40-46 | 50-150 |
| VWF RCo, % | 100-115 | 46-55 | 50-150 |
| VWF:HMW multimers | Absent | Absent | Yes |
| Blood group | A+ | O+ | — |
| RIPA, mg/mL | 0.25 | 0.25 | 1-1.5 |
| Prothrombin consumption, % | 32 | 32 | < 10 |
| ADAMTS 13, % | 100 | 100 | 80-150 |
. | Patient 1 . | Patient 2 . | Controls . |
|---|---|---|---|
| Platelet count, × 109/L | < 20 | < 20 | 150-400 |
| Platelet volume, μm3 | 8.5 | 8.5 | 6-8 |
| Platelet agglutinates | + | + | No |
| VWF Ag, % | 75-100 | 40-46 | 50-150 |
| VWF RCo, % | 100-115 | 46-55 | 50-150 |
| VWF:HMW multimers | Absent | Absent | Yes |
| Blood group | A+ | O+ | — |
| RIPA, mg/mL | 0.25 | 0.25 | 1-1.5 |
| Prothrombin consumption, % | 32 | 32 | < 10 |
| ADAMTS 13, % | 100 | 100 | 80-150 |
HMW indicates high-molecular-weight multimers; +, present; No, absent; and —, not matched