Table 6

Autoimmune manifestations after HSCT

Donor group, no. patientsAutoimmunity disease score before HSCTChimerismAutoimmune manifestations after HSCT
MSD    
    1 5, AIHA, thrombocytopenia Full Thrombocytopenia* 
    2 Full Thrombocytopenia* 
    3 Full Autoimmune hypothyroidism 
    4 Mixed/split Thrombocytopenia, autoimmune hypothyroidism* 
    5 Full Addison disease 
URD    
    1 5, AIHA Mixed Inflammatory bowel disease (plus 6 mo after HSCT until 5 y) 
    2 Mixed Thrombocytopenia* 
    3 Split Autoimmune hypothyroidism 
    4 Full Thrombocytopenia* 
    5 Mixed Neutropenia, thrombocytopenia* 
    6 5, vasculitis Mixed Vasculitis 
    7 5, aortic vasculitis Full Pericarditis, AIHA 
    8 Mixed Autoimmune hypothyroidism 
    9 Mixed Thrombocytopenia* 
MMRD    
    1 5, AIHA, thrombocytopenia Mixed AIHA 
    2 5, AIHA, thrombocytopenia Mixed Thrombocytopenia* 
    3 5, AIHA, thrombocytopenia Mixed AIHA, thrombocytopenia* 
    4 Mixed Vasculitis 
    5 Mixed Thrombocytopenia* 
Donor group, no. patientsAutoimmunity disease score before HSCTChimerismAutoimmune manifestations after HSCT
MSD    
    1 5, AIHA, thrombocytopenia Full Thrombocytopenia* 
    2 Full Thrombocytopenia* 
    3 Full Autoimmune hypothyroidism 
    4 Mixed/split Thrombocytopenia, autoimmune hypothyroidism* 
    5 Full Addison disease 
URD    
    1 5, AIHA Mixed Inflammatory bowel disease (plus 6 mo after HSCT until 5 y) 
    2 Mixed Thrombocytopenia* 
    3 Split Autoimmune hypothyroidism 
    4 Full Thrombocytopenia* 
    5 Mixed Neutropenia, thrombocytopenia* 
    6 5, vasculitis Mixed Vasculitis 
    7 5, aortic vasculitis Full Pericarditis, AIHA 
    8 Mixed Autoimmune hypothyroidism 
    9 Mixed Thrombocytopenia* 
MMRD    
    1 5, AIHA, thrombocytopenia Mixed AIHA 
    2 5, AIHA, thrombocytopenia Mixed Thrombocytopenia* 
    3 5, AIHA, thrombocytopenia Mixed AIHA, thrombocytopenia* 
    4 Mixed Vasculitis 
    5 Mixed Thrombocytopenia* 

AIHA indicates autoimmune hemolytic anemia.

*

Mean platelet volume: normal, detection of antiplatelet antibodies.

Splenectomy 20 and 19 months following HSCT, respectively.

Split chimerism.

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