Table 1 Clinical and biological features... | American Society of Hematology

Table 1

Clinical and biological features of β-thalassemic patients

	β genotype	α genotype	Splenectomy	Transfusions
β-TI patients
1	IVSI-110/IVSI-110	−α^3.7α/αα	yes	<4 wks
2	β⁰39/δβ ″sicilian type″	—	yes	no
3	β⁰39/+22	—	no	no
4	IVSI-6/IVSI-6	—	yes	>4 wks
5	β⁰39/β⁰39	−α^3.7α/−α^3.7 α	yes	<4 wks
6	IVSI-6/IVSI-6	—	yes	>4 wks
7	β⁰39	ααα	yes	>4 wks
8	β⁰39	ααα	yes	<4 wks
9	IVSI-1/IVSI-6	—	yes	>4 wks
10	−87/−87	—	yes	no
β-TM patients
1	β⁰39/β⁰39	—	yes	Every 3 wks
2	β⁰39/β⁰39	—	yes	Every 3 wks
3	β⁰39/β⁰39	—	yes	Every 3 wks
4	β⁰39/β⁰39	—	yes	Every 3 wks
5	β⁰39/β⁰39	—	no	Every 3 wks
6	β⁰39/β⁰39	—	yes	Every 3 wks
7	β⁰39/β⁰39	—	yes	Every 3 wks
8	β⁰39/β⁰39	—	yes	Every 3 wks
9	β⁰39/β⁰39	—	yes	Every 3 wks
10	β⁰39/β⁰39	—	yes	Every 3 wks

	β genotype	α genotype	Splenectomy	Transfusions
β-TI patients
1	IVSI-110/IVSI-110	−α^3.7α/αα	yes	<4 wks
2	β⁰39/δβ ″sicilian type″	—	yes	no
3	β⁰39/+22	—	no	no
4	IVSI-6/IVSI-6	—	yes	>4 wks
5	β⁰39/β⁰39	−α^3.7α/−α^3.7 α	yes	<4 wks
6	IVSI-6/IVSI-6	—	yes	>4 wks
7	β⁰39	ααα	yes	>4 wks
8	β⁰39	ααα	yes	<4 wks
9	IVSI-1/IVSI-6	—	yes	>4 wks
10	−87/−87	—	yes	no
β-TM patients
1	β⁰39/β⁰39	—	yes	Every 3 wks
2	β⁰39/β⁰39	—	yes	Every 3 wks
3	β⁰39/β⁰39	—	yes	Every 3 wks
4	β⁰39/β⁰39	—	yes	Every 3 wks
5	β⁰39/β⁰39	—	no	Every 3 wks
6	β⁰39/β⁰39	—	yes	Every 3 wks
7	β⁰39/β⁰39	—	yes	Every 3 wks
8	β⁰39/β⁰39	—	yes	Every 3 wks
9	β⁰39/β⁰39	—	yes	Every 3 wks
10	β⁰39/β⁰39	—	yes	Every 3 wks

Hb was 100 to 105 g/L for all patients listed. Either the time interval since the last transfusion or the rate of transfusion is shown in column 5.

— indicates normal α genotype.