Table 5.

Therapy of acute attacks of porphyria.

  • Remove inciting factors: alcohol, drugs, toxins, chemicals

  • Nutritional supplementation: at least 300 grams glucose/day

  • Frequent checks of neurologic status: especially watch for development of paresis of muscles of respiration

  • Monitor for hypoventilation (rising arterial PpCO2), hyponatremia, or hypomagnesemia and treat vigorously if found

  • Intravenous heme: 3–4 mg/kg/day for 3–5 days

  • Parenteral meperidine or morphine for pain

  • Phenothiazines for nausea, vomiting, agitation, etc.

  • Propranolol or nadolol for tachycardia, hypertension

 
  • Remove inciting factors: alcohol, drugs, toxins, chemicals

  • Nutritional supplementation: at least 300 grams glucose/day

  • Frequent checks of neurologic status: especially watch for development of paresis of muscles of respiration

  • Monitor for hypoventilation (rising arterial PpCO2), hyponatremia, or hypomagnesemia and treat vigorously if found

  • Intravenous heme: 3–4 mg/kg/day for 3–5 days

  • Parenteral meperidine or morphine for pain

  • Phenothiazines for nausea, vomiting, agitation, etc.

  • Propranolol or nadolol for tachycardia, hypertension

 
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