Table 1A.

Classification of the porphyrias.

1. According to Sites of Major Overproduction of Porphyrins and Porphyrin Precursors
ErythropoieticHepatic
CEP Acute, Inducible 
EPP ADP 
 AIP 
 HCP 
 VP 
 Chronic 
 PCT 
 HEP 
1. According to Sites of Major Overproduction of Porphyrins and Porphyrin Precursors
ErythropoieticHepatic
CEP Acute, Inducible 
EPP ADP 
 AIP 
 HCP 
 VP 
 Chronic 
 PCT 
 HEP 
2. According to Major Clinical Manifestations
Abdominal pain (neurovisceral)Cutaneous (photosensitivity, damage)
Abbreviations: CEP, congenital erythropoietic (Uro) porphyria; EP, erythropoietic protoporphyria; ADP, ALA dehydratase deficiency porphyia; AIP, acute intermittent porphyria; HCP, hereditary coproporphyria; VP, variegate porphyria; PCT, porphyria cutanea tarda; HEP, hepatoerythropoietic porphyria. 
ADP CEP 
AIP EPP 
HCP HCP 
VP HEP 
 PCT 
 VP 
2. According to Major Clinical Manifestations
Abdominal pain (neurovisceral)Cutaneous (photosensitivity, damage)
Abbreviations: CEP, congenital erythropoietic (Uro) porphyria; EP, erythropoietic protoporphyria; ADP, ALA dehydratase deficiency porphyia; AIP, acute intermittent porphyria; HCP, hereditary coproporphyria; VP, variegate porphyria; PCT, porphyria cutanea tarda; HEP, hepatoerythropoietic porphyria. 
ADP CEP 
AIP EPP 
HCP HCP 
VP HEP 
 PCT 
 VP 
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