Classification of the porphyrias.
1. According to Sites of Major Overproduction of Porphyrins and Porphyrin Precursors . | |
---|---|
Erythropoietic . | Hepatic . |
CEP | Acute, Inducible |
EPP | ADP |
AIP | |
HCP | |
VP | |
Chronic | |
PCT | |
HEP |
1. According to Sites of Major Overproduction of Porphyrins and Porphyrin Precursors . | |
---|---|
Erythropoietic . | Hepatic . |
CEP | Acute, Inducible |
EPP | ADP |
AIP | |
HCP | |
VP | |
Chronic | |
PCT | |
HEP |
2. According to Major Clinical Manifestations . | |
---|---|
Abdominal pain (neurovisceral) . | Cutaneous (photosensitivity, damage) . |
Abbreviations: CEP, congenital erythropoietic (Uro) porphyria; EP, erythropoietic protoporphyria; ADP, ALA dehydratase deficiency porphyia; AIP, acute intermittent porphyria; HCP, hereditary coproporphyria; VP, variegate porphyria; PCT, porphyria cutanea tarda; HEP, hepatoerythropoietic porphyria. | |
ADP | CEP |
AIP | EPP |
HCP | HCP |
VP | HEP |
PCT | |
VP |
2. According to Major Clinical Manifestations . | |
---|---|
Abdominal pain (neurovisceral) . | Cutaneous (photosensitivity, damage) . |
Abbreviations: CEP, congenital erythropoietic (Uro) porphyria; EP, erythropoietic protoporphyria; ADP, ALA dehydratase deficiency porphyia; AIP, acute intermittent porphyria; HCP, hereditary coproporphyria; VP, variegate porphyria; PCT, porphyria cutanea tarda; HEP, hepatoerythropoietic porphyria. | |
ADP | CEP |
AIP | EPP |
HCP | HCP |
VP | HEP |
PCT | |
VP |