Table 1.

Summary of patients with TDT and transfusion characteristics

Patients with TDT 
Patients, N 36 
Age, y 48.75 (44.91-52.59) 
Sex, male/female 13/23 
Body mass index 23.35 (22.51-24.18) 
Smoking, n 10 
ABO 14A, 6B, 16O 
Rhesus, +/− 33/3 
β++++ or β+++ (mild deficiency), n 10 
β++ or β0++ (moderate deficiency), n 18 
β0+ or β00 (severe deficiency), n 7  
Extramedullary hematopoiesis, yes/no 11/25 
Splenectomy, yes/no 22/14 
Cholecystectomy, yes/no 17/19 
Hypogonadism, yes/no 17/19 
Hypothyroidism, yes/no 14/22 
Osteopenia, yes/no 12/24 
Osteoporosis, yes/no 17/19 
Pulmonary hypertension, yes/no 7/29 
Atrial fibrillation, yes/no 8/28 
Ferriprox, n 11 
Exjade, n 10 
Desferal, n 
Ferriprox and Desferal, n 
Ferriprox and Exjade, n 
No chelation, n 
Age of first transfusion, y 16.06 (8.45-23.66) 
Duration of transfusion therapy, y 32.67 (26.42-38.91) 
Interval since previous transfusion, d 18.42 (16.03-20.80) 
Average transfusion interval, d 16.75 (15.63-17.87) 
Units per transfusion, n 1 unit, 13; 2 units, 23 
Donors and RBC units 
Donors/units, N 58 
Age, y 43.26 (40.80-45.72) 
Sex, male/female 45/13 
First-time donors, n 10 
Storage age, d 9.39 (7.42-11.36) 
Total volume transfused, mL 537.5 (480.4-594.6) 
RBC unit Hb, g 92.73 (83.33-102.1) 
Patients with TDT 
Patients, N 36 
Age, y 48.75 (44.91-52.59) 
Sex, male/female 13/23 
Body mass index 23.35 (22.51-24.18) 
Smoking, n 10 
ABO 14A, 6B, 16O 
Rhesus, +/− 33/3 
β++++ or β+++ (mild deficiency), n 10 
β++ or β0++ (moderate deficiency), n 18 
β0+ or β00 (severe deficiency), n 7  
Extramedullary hematopoiesis, yes/no 11/25 
Splenectomy, yes/no 22/14 
Cholecystectomy, yes/no 17/19 
Hypogonadism, yes/no 17/19 
Hypothyroidism, yes/no 14/22 
Osteopenia, yes/no 12/24 
Osteoporosis, yes/no 17/19 
Pulmonary hypertension, yes/no 7/29 
Atrial fibrillation, yes/no 8/28 
Ferriprox, n 11 
Exjade, n 10 
Desferal, n 
Ferriprox and Desferal, n 
Ferriprox and Exjade, n 
No chelation, n 
Age of first transfusion, y 16.06 (8.45-23.66) 
Duration of transfusion therapy, y 32.67 (26.42-38.91) 
Interval since previous transfusion, d 18.42 (16.03-20.80) 
Average transfusion interval, d 16.75 (15.63-17.87) 
Units per transfusion, n 1 unit, 13; 2 units, 23 
Donors and RBC units 
Donors/units, N 58 
Age, y 43.26 (40.80-45.72) 
Sex, male/female 45/13 
First-time donors, n 10 
Storage age, d 9.39 (7.42-11.36) 
Total volume transfused, mL 537.5 (480.4-594.6) 
RBC unit Hb, g 92.73 (83.33-102.1) 

Arithmetic mean (95% CI) (lower to upper 95% CI of mean).

CI, confidence interval.

In 1 patient, diagnosis was based on Hb analysis by high-performance liquid chromatography.

In 1-unit and 2-unit events.

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