Table 1.

Patient demographics and baseline characteristics

CharacteristicN = 15
Mean age (range), y 39 (25-57) 
Sex, n (%)  
Female 5 (33.3) 
Male 10 (66.7) 
African or African American race, n (%) 15 (100) 
HbSS genotype, n (%) 15 (100) 
HU use, n (%) 11 (73.3) 
l-Glutamine use, n (%) 0 (0.0) 
Baseline laboratory measures  
Mean Hb (SD), g/dL 8.80 (0.99) 
Mean absolute reticulocyte count (SD), ×103/μL 217.21 (88.27) 
Mean total bilirubin (SD), mg/dL 2.73 (1.43) 
Mean lactate dehydrogenase (SD), U/L 536.71 (222.16) 
Median HbF (25th, 75th percentile), % 13.80 (7.40, 23.95) 
CharacteristicN = 15
Mean age (range), y 39 (25-57) 
Sex, n (%)  
Female 5 (33.3) 
Male 10 (66.7) 
African or African American race, n (%) 15 (100) 
HbSS genotype, n (%) 15 (100) 
HU use, n (%) 11 (73.3) 
l-Glutamine use, n (%) 0 (0.0) 
Baseline laboratory measures  
Mean Hb (SD), g/dL 8.80 (0.99) 
Mean absolute reticulocyte count (SD), ×103/μL 217.21 (88.27) 
Mean total bilirubin (SD), mg/dL 2.73 (1.43) 
Mean lactate dehydrogenase (SD), U/L 536.71 (222.16) 
Median HbF (25th, 75th percentile), % 13.80 (7.40, 23.95) 

HbF, fetal Hb; SD, standard deviation.

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