Prevalence of coagulation factor deficiency and low coagulation factor levels according to hemophilia type and severity
. | HA . | HB . | P value . |
---|---|---|---|
Minimum factor level, <40 IU/dL | |||
Severity in family | |||
Carriers | 42/183 (23.0%) | 23/78 (29.5%) | |
Severe | 20/97 (20.6%) | 8/27 (29.6%) | |
Moderate | 5/18 (27.8%) | 12/31 (38.7%) | |
Mild | 17/68 (25.0%) | 3/20 (15.0%) | |
P = .706 | P = .193 | ||
Noncarriers | 0/57 (0.0%) | 0/22 (0.0%) | |
P value | <.001 | .004 | .264 |
Minimum factor level, <50 IU/dL | |||
Severity in family | |||
Carriers | 65/183 (35.5%) | 32/78 (41.0%) | |
Severe | 34/97 (35.1%) | 11/27 (40.7%) | |
Moderate | 7/18 (38.9%) | 15/31 (48.4%) | |
Mild | 24/68 (35.3%) | 6/20 (30.0%) | |
P = .951 | P = .427 | ||
Noncarriers | 1/57 (1.8%) | 1/22 (4.5%) | |
P value | <.001 | .001 | .399 |
. | HA . | HB . | P value . |
---|---|---|---|
Minimum factor level, <40 IU/dL | |||
Severity in family | |||
Carriers | 42/183 (23.0%) | 23/78 (29.5%) | |
Severe | 20/97 (20.6%) | 8/27 (29.6%) | |
Moderate | 5/18 (27.8%) | 12/31 (38.7%) | |
Mild | 17/68 (25.0%) | 3/20 (15.0%) | |
P = .706 | P = .193 | ||
Noncarriers | 0/57 (0.0%) | 0/22 (0.0%) | |
P value | <.001 | .004 | .264 |
Minimum factor level, <50 IU/dL | |||
Severity in family | |||
Carriers | 65/183 (35.5%) | 32/78 (41.0%) | |
Severe | 34/97 (35.1%) | 11/27 (40.7%) | |
Moderate | 7/18 (38.9%) | 15/31 (48.4%) | |
Mild | 24/68 (35.3%) | 6/20 (30.0%) | |
P = .951 | P = .427 | ||
Noncarriers | 1/57 (1.8%) | 1/22 (4.5%) | |
P value | <.001 | .001 | .399 |