Table 4.

Prevalence of coagulation factor deficiency and low coagulation factor levels according to hemophilia type and severity

HAHBP value
Minimum factor level, <40 IU/dL    
Severity in family    
Carriers 42/183 (23.0%) 23/78 (29.5%)  
Severe 20/97 (20.6%) 8/27 (29.6%)  
Moderate 5/18 (27.8%) 12/31 (38.7%)  
Mild 17/68 (25.0%) 3/20 (15.0%)  
 P = .706 P = .193  
Noncarriers 0/57 (0.0%) 0/22 (0.0%)  
P value <.001 .004 .264 
Minimum factor level, <50 IU/dL    
Severity in family    
Carriers 65/183 (35.5%) 32/78 (41.0%)  
Severe 34/97 (35.1%) 11/27 (40.7%)  
Moderate 7/18 (38.9%) 15/31 (48.4%)  
Mild 24/68 (35.3%) 6/20 (30.0%)  
 P = .951 P = .427  
Noncarriers 1/57 (1.8%) 1/22 (4.5%)  
P value <.001 .001 .399 
HAHBP value
Minimum factor level, <40 IU/dL    
Severity in family    
Carriers 42/183 (23.0%) 23/78 (29.5%)  
Severe 20/97 (20.6%) 8/27 (29.6%)  
Moderate 5/18 (27.8%) 12/31 (38.7%)  
Mild 17/68 (25.0%) 3/20 (15.0%)  
 P = .706 P = .193  
Noncarriers 0/57 (0.0%) 0/22 (0.0%)  
P value <.001 .004 .264 
Minimum factor level, <50 IU/dL    
Severity in family    
Carriers 65/183 (35.5%) 32/78 (41.0%)  
Severe 34/97 (35.1%) 11/27 (40.7%)  
Moderate 7/18 (38.9%) 15/31 (48.4%)  
Mild 24/68 (35.3%) 6/20 (30.0%)  
 P = .951 P = .427  
Noncarriers 1/57 (1.8%) 1/22 (4.5%)  
P value <.001 .001 .399 
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