Table 2.

Characteristics of participants with SCD

Pre-HSCT (SCD)Post-HSCT
Total N (%) 
Sex   
Male 2 (33%) 4 (80%) 
Female 4 (67%) 1 (20%) 
Age (median, range) 41.5 (26-61) 31 (19-54) 
Hydroxyrea use (at time of study) 4 (67%) 
Type of transplant   
Matched related donor NA 3 (60%) 
Haploidentitical NA 2 (40%) 
Stem cell donor genotype   
AS NA 4 (80%) 
AA NA 1 (20%) 
Chimerism at time of enrollment   
Full DMC NA 3 (60%) 
Mixed DMC NA 2 (40%) 
Hematologic data, average   
WBC (K/mcL) 8.9 6.9 
RBC (M/mcL) 4.1 
Hemoglobin (g/dL) 8.9 12.4 
Hematocrit (%) 25.2 36.6 
MCV (fL) 86 90.2 
Platelet count (K/mcL) 406.4 277 
ARC (K/mcL) 191.6 175 
HbF (%) 10.2 
HbA (%) 56.8 
HbA2 (%) 3.7 3.1 
HbS (%) 68.8 39.1 
HbC (%) 43.3 NA 
AST (U/L) 26.3 27.5 
Total bilirubin (mg/dL) 1.7 1.2 
LDH (U/L) 324.9 271.5 
Time from transplant mean ± SD (mo) NA 29.8 ± 17.3 
Pre-HSCT (SCD)Post-HSCT
Total N (%) 
Sex   
Male 2 (33%) 4 (80%) 
Female 4 (67%) 1 (20%) 
Age (median, range) 41.5 (26-61) 31 (19-54) 
Hydroxyrea use (at time of study) 4 (67%) 
Type of transplant   
Matched related donor NA 3 (60%) 
Haploidentitical NA 2 (40%) 
Stem cell donor genotype   
AS NA 4 (80%) 
AA NA 1 (20%) 
Chimerism at time of enrollment   
Full DMC NA 3 (60%) 
Mixed DMC NA 2 (40%) 
Hematologic data, average   
WBC (K/mcL) 8.9 6.9 
RBC (M/mcL) 4.1 
Hemoglobin (g/dL) 8.9 12.4 
Hematocrit (%) 25.2 36.6 
MCV (fL) 86 90.2 
Platelet count (K/mcL) 406.4 277 
ARC (K/mcL) 191.6 175 
HbF (%) 10.2 
HbA (%) 56.8 
HbA2 (%) 3.7 3.1 
HbS (%) 68.8 39.1 
HbC (%) 43.3 NA 
AST (U/L) 26.3 27.5 
Total bilirubin (mg/dL) 1.7 1.2 
LDH (U/L) 324.9 271.5 
Time from transplant mean ± SD (mo) NA 29.8 ± 17.3 

AST, aspartate transaminase; HbA, adult hemoglobin; HbA2, hemoglobin A2; HbC, hemoglobin C; HbS, sickle hemoglobin; MCV, mean corpuscular volume; TBI, total body irradiation; WBC, white blood cell count.

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