Table 1.

Annual incidence of malignancy-associated HLH per health care region overall and in adults from 2012 to 2018 per 100 000 individuals in “diagnosis code-based possible malignancy-associated HLH” and “probable malignancy-associated HLH”

Health care regionIncidenceCasesMean population 31 December 2012-2018
”Diagnosis code-based possible malignancy associated HLH” (n = 249) 
Stockholm    
Total 0.55 89 2 292 250 
Adults 0.71 89 1 795 693 
South East    
Total 0.39 28 1 035 005 
Adults 0.48 28 824 810 
South (excluding Halland)    
Total 0.51 59 1 657 096 
Adults 0.63 58 1 313 444 
West (including Halland)    
Total 0.27 37 1 968 503 
Adults 0.32 35 1 562 747 
Mid Sweden    
Total 0.19 27 2 038 479 
Adults 0.24 27 1 629 897 
North    
Total 0.15 886 482 
Adults 0.18 716 320 
”Probable malignancy-associated HLH” from −90 days to +365 days in relation to the cancer diagnosis (n = 146) 
Stockholm    
Total 0.30 48 2 292 250 
Adults 0.38 48 1 795 693 
South East    
Total 0.28 20 1 035 005 
Adults 0.35 20 824 810 
South (excluding Halland)    
Total 0.28 32 1 657 096 
Adults 0.35 31 1 313 444 
West (including Halland)    
Total 0.17 24 1 968 503 
Adults 0.21 23 1 562 747 
Mid Sweden    
Total 0.11 15 2 038 479 
Adults 0.14 15 1 629 897 
North    
Total 0.11 886 482 
Adults 0.14 716 320 
Health care regionIncidenceCasesMean population 31 December 2012-2018
”Diagnosis code-based possible malignancy associated HLH” (n = 249) 
Stockholm    
Total 0.55 89 2 292 250 
Adults 0.71 89 1 795 693 
South East    
Total 0.39 28 1 035 005 
Adults 0.48 28 824 810 
South (excluding Halland)    
Total 0.51 59 1 657 096 
Adults 0.63 58 1 313 444 
West (including Halland)    
Total 0.27 37 1 968 503 
Adults 0.32 35 1 562 747 
Mid Sweden    
Total 0.19 27 2 038 479 
Adults 0.24 27 1 629 897 
North    
Total 0.15 886 482 
Adults 0.18 716 320 
”Probable malignancy-associated HLH” from −90 days to +365 days in relation to the cancer diagnosis (n = 146) 
Stockholm    
Total 0.30 48 2 292 250 
Adults 0.38 48 1 795 693 
South East    
Total 0.28 20 1 035 005 
Adults 0.35 20 824 810 
South (excluding Halland)    
Total 0.28 32 1 657 096 
Adults 0.35 31 1 313 444 
West (including Halland)    
Total 0.17 24 1 968 503 
Adults 0.21 23 1 562 747 
Mid Sweden    
Total 0.11 15 2 038 479 
Adults 0.14 15 1 629 897 
North    
Total 0.11 886 482 
Adults 0.14 716 320 
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