Table 4.

Therapies employed in patients with PCH

TherapyPatients (n = 229) 
None 72 
Steroids 57 
Antimicrobials 13 
Steroids, antimicrobials 
Steroids, IVIG 
Steroids, rituximab 
Steroids, CHOP 
Steroids, azathioprine 
Steroids, chlorambucil 
Antimicrobials, IVIG 
Rituximab 
Rituximab, fludarabine, cyclophosphamide, danazol 
Steroids, androgen therapy 
Steroids, antimicrobials, IVIG 
Steroids, azathioprine, rituximab 
Steroids, cyclophosphamide, rituximab 
Steroids, danazol 
Steroids, eculizumab, antimicrobials 
Steroids, eculizumab, antimicrobials, TPE 
Steroids, eculizumab, cyclophosphamide 
Steroids, IVIG, antimicrobials 
Steroids, IVIG, rituximab 
Steroids, IVIG, TPE 
Steroids, rituximab, cyclophosphamide 
Steroids, TPE 
TPE 
TherapyPatients (n = 229) 
None 72 
Steroids 57 
Antimicrobials 13 
Steroids, antimicrobials 
Steroids, IVIG 
Steroids, rituximab 
Steroids, CHOP 
Steroids, azathioprine 
Steroids, chlorambucil 
Antimicrobials, IVIG 
Rituximab 
Rituximab, fludarabine, cyclophosphamide, danazol 
Steroids, androgen therapy 
Steroids, antimicrobials, IVIG 
Steroids, azathioprine, rituximab 
Steroids, cyclophosphamide, rituximab 
Steroids, danazol 
Steroids, eculizumab, antimicrobials 
Steroids, eculizumab, antimicrobials, TPE 
Steroids, eculizumab, cyclophosphamide 
Steroids, IVIG, antimicrobials 
Steroids, IVIG, rituximab 
Steroids, IVIG, TPE 
Steroids, rituximab, cyclophosphamide 
Steroids, TPE 
TPE 

CHOP, cyclophosphamide, hydroxydaunorubicin, oncovin, prednisone; IVIG, intravenous immunoglobulin; TPE, therapeutic plasma exchange.

Therapy was not reported for 47 patients.

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