Table 3.

Clinical outcomes following allogeneic transplantation for HLH

Clinical OutcomeEstimate, % (95% CI)
aGVHD 
Grade 2-4 at 6 mo 29 (11-49) 
Grade 2-4 at 1 y 38 (18-58) 
Grade 3-4 at 6 mo 9.5 (1.5-27) 
cGVHD 
All cGVHD at 2 y 52 (29-71) 
Moderate/severe cGVHD at 2 y 29 (11-49) 
Relapse incidence at 3 y 15 (3.4-33) 
Nonrelapse mortality at 3 y 15 (3.5-34) 
PFS at 3 y 71 (46-86) 
OS at 3 y 75 (51-89) 
Clinical OutcomeEstimate, % (95% CI)
aGVHD 
Grade 2-4 at 6 mo 29 (11-49) 
Grade 2-4 at 1 y 38 (18-58) 
Grade 3-4 at 6 mo 9.5 (1.5-27) 
cGVHD 
All cGVHD at 2 y 52 (29-71) 
Moderate/severe cGVHD at 2 y 29 (11-49) 
Relapse incidence at 3 y 15 (3.4-33) 
Nonrelapse mortality at 3 y 15 (3.5-34) 
PFS at 3 y 71 (46-86) 
OS at 3 y 75 (51-89) 

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