Clinical characterization of IEI patients with lymphoma
. | CVID . | APDS . | DNA repair deficiency . | P value CVID vs APDS . | P value CVID vs DNA repair deficiency . | P value APDS vs DNA repair deficiency . |
---|---|---|---|---|---|---|
No. of patients | 14 | 4 | 5 | |||
Sex | 0.2745† | 0.1409† | 1.0000† | |||
Male (%) | 9 (64%) | 1 (25%) | 1 (20%) | |||
Female (%) | 5 (36%) | 3 (75%) | 4 (80%) | |||
EBV status | 1.0000† | 0.1409† | 0.5238† | |||
Positive (%) | 5 (36%) | 2 (50%) | 4 (80%) | |||
Negative (%) | 9 (64%) | 2 (50%) | 1 (20%) | |||
Average IEI onset age (range), y | 42 (5-66)* | 1 (1-2) | 7 (1-14) | 0.0008‡ | 0.0016‡ | 0.4127‡ |
Average lymphoma onset age (range), y | 50 (17-77) | 19 (16-20) | 11 (2-18) | 0.0046‡ | 0.0003‡ | 0.0317‡ |
. | CVID . | APDS . | DNA repair deficiency . | P value CVID vs APDS . | P value CVID vs DNA repair deficiency . | P value APDS vs DNA repair deficiency . |
---|---|---|---|---|---|---|
No. of patients | 14 | 4 | 5 | |||
Sex | 0.2745† | 0.1409† | 1.0000† | |||
Male (%) | 9 (64%) | 1 (25%) | 1 (20%) | |||
Female (%) | 5 (36%) | 3 (75%) | 4 (80%) | |||
EBV status | 1.0000† | 0.1409† | 0.5238† | |||
Positive (%) | 5 (36%) | 2 (50%) | 4 (80%) | |||
Negative (%) | 9 (64%) | 2 (50%) | 1 (20%) | |||
Average IEI onset age (range), y | 42 (5-66)* | 1 (1-2) | 7 (1-14) | 0.0008‡ | 0.0016‡ | 0.4127‡ |
Average lymphoma onset age (range), y | 50 (17-77) | 19 (16-20) | 11 (2-18) | 0.0046‡ | 0.0003‡ | 0.0317‡ |