World Health Organization and EORTC classification of PCLs
| Classification . |
|---|
| Cutaneous T-cell and NK-cell lymphomas |
| Mycosis fungoides |
| MF variants and subtypes |
| Folliculotropic MF |
| Pagetoid reticulosis |
| Granulomatous slack skin |
| Sézary syndrome |
| Primary cutaneous CD30+ lymphoproliferative disorders |
| Primary cutaneous anaplastic large cell lymphoma |
| Lymphomatoid papulosis |
| Adult T-cell leukemia/lymphoma |
| Subcutaneous panniculitis–like T-cell lymphoma |
| Extranodal NK/T-cell lymphoma, nasal type |
| Chronic active EBV infection |
| Primary cutaneous peripheral T-cell lymphoma, rare subtypes |
| Primary cutaneous γ/δ T-cell lymphoma |
| Primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma (provisional) |
| Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder (provisional) |
| Primary cutaneous acral CD8+ T-cell lymphoma (provisional) |
| Primary cutaneous peripheral T-cell lymphoma, NOS |
| Cutaneous B-cell lymphomas |
| Primary cutaneous marginal zone lymphoma |
| Primary cutaneous follicle center lymphoma |
| Primary cutaneous diffuse large B-cell lymphoma, leg type |
| EBV+ mucocutaneous ulcer (provisional) |
| Intravascular large B-cell lymphoma |
| Classification . |
|---|
| Cutaneous T-cell and NK-cell lymphomas |
| Mycosis fungoides |
| MF variants and subtypes |
| Folliculotropic MF |
| Pagetoid reticulosis |
| Granulomatous slack skin |
| Sézary syndrome |
| Primary cutaneous CD30+ lymphoproliferative disorders |
| Primary cutaneous anaplastic large cell lymphoma |
| Lymphomatoid papulosis |
| Adult T-cell leukemia/lymphoma |
| Subcutaneous panniculitis–like T-cell lymphoma |
| Extranodal NK/T-cell lymphoma, nasal type |
| Chronic active EBV infection |
| Primary cutaneous peripheral T-cell lymphoma, rare subtypes |
| Primary cutaneous γ/δ T-cell lymphoma |
| Primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma (provisional) |
| Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder (provisional) |
| Primary cutaneous acral CD8+ T-cell lymphoma (provisional) |
| Primary cutaneous peripheral T-cell lymphoma, NOS |
| Cutaneous B-cell lymphomas |
| Primary cutaneous marginal zone lymphoma |
| Primary cutaneous follicle center lymphoma |
| Primary cutaneous diffuse large B-cell lymphoma, leg type |
| EBV+ mucocutaneous ulcer (provisional) |
| Intravascular large B-cell lymphoma |
Based on Willemze et al.2
NK, natural killer; EBV, Epstein-Barr virus.