VWF(Ag)/ADAMTS13 ratios and exercise test results in 18 patients who had repeat assessments performed over time
| Patient . | Assessment . | VWF(Ag)/ ADAMTS13 ratio . | Exercise test result . | 
|---|---|---|---|
| 1 | Baseline | 1.5 | Lactate increase 0.8-2.4 | 
| 1 mo | 1.5 | Lactate increase and desaturation 3% | |
| 2 | Baseline | 1.7 | Lactate increase 0.5-2.4 and desaturation 8% | 
| 1 mo | 1.5 | Desaturation 3% | |
| 3 | Baseline | 1.2 | Not done | 
| 2 mo | 1.3 | Not done | |
| 4 | Baseline | 1.2 | Normal | 
| 1 mo | 1.0 | Desaturation 3% | |
| 5 | Baseline | 1.3 | Normal | 
| 5 mo | 1.4 | Not done | |
| 6 | Baseline | 0.6 | Lactate increase 0.9-6.9 | 
| 4 mo | 0.7 | Not done | |
| 7 | Baseline | 1.2 | Normal | 
| 1 mo | 1.0 | Normal | |
| 8 | Baseline | 1.3 | Normal | 
| 1 mo | 1.5 | Desaturation 3% | |
| 4 mo | 1.3 | Not done | |
| 9 | Baseline | 1.7 | Desaturation 13% and lactate increase 2.6-7.3 | 
| 1 mo | 1.7 | Desaturation 9% and lactate increase 0.5-8.7 | |
| 10 | Baseline | 1.5 | Normal | 
| 6 mo | 1.3 | Normal | |
| 11 | Baseline | 1.1 | Normal | 
| 3 mo | 1.1 | Not done | |
| 12 | Baseline | 0.9 | Normal | 
| 1 mo | 0.9 | Not done | |
| 13 | Baseline | 3.5 | Normal | 
| 3 mo | 3.6 | Not done | |
| 14 | Baseline | 1.9 | Normal | 
| 1 mo | 0.7 | Normal | |
| 2 mo | 0.9 | Not done | |
| 15 | Baseline | 2.0 | Desaturation 3% and lactate increase 0.8-2.4 | 
| 2 mo | 1.7 | Normal | |
| 3 mo | 1.6 | Not done | |
| 5 mo | 1.7 | Not done | |
| 16 | Baseline | 1.5 | Normal | 
| 6 mo | 1.4 | Normal | |
| 17 | Baseline | 0.5 | Normal | 
| 6 mo | 0.4 | Not done | |
| 18 | Baseline | 2.8 | Not done | 
| 4 mo | 1.8 | Not done | 
| Patient . | Assessment . | VWF(Ag)/ ADAMTS13 ratio . | Exercise test result . | 
|---|---|---|---|
| 1 | Baseline | 1.5 | Lactate increase 0.8-2.4 | 
| 1 mo | 1.5 | Lactate increase and desaturation 3% | |
| 2 | Baseline | 1.7 | Lactate increase 0.5-2.4 and desaturation 8% | 
| 1 mo | 1.5 | Desaturation 3% | |
| 3 | Baseline | 1.2 | Not done | 
| 2 mo | 1.3 | Not done | |
| 4 | Baseline | 1.2 | Normal | 
| 1 mo | 1.0 | Desaturation 3% | |
| 5 | Baseline | 1.3 | Normal | 
| 5 mo | 1.4 | Not done | |
| 6 | Baseline | 0.6 | Lactate increase 0.9-6.9 | 
| 4 mo | 0.7 | Not done | |
| 7 | Baseline | 1.2 | Normal | 
| 1 mo | 1.0 | Normal | |
| 8 | Baseline | 1.3 | Normal | 
| 1 mo | 1.5 | Desaturation 3% | |
| 4 mo | 1.3 | Not done | |
| 9 | Baseline | 1.7 | Desaturation 13% and lactate increase 2.6-7.3 | 
| 1 mo | 1.7 | Desaturation 9% and lactate increase 0.5-8.7 | |
| 10 | Baseline | 1.5 | Normal | 
| 6 mo | 1.3 | Normal | |
| 11 | Baseline | 1.1 | Normal | 
| 3 mo | 1.1 | Not done | |
| 12 | Baseline | 0.9 | Normal | 
| 1 mo | 0.9 | Not done | |
| 13 | Baseline | 3.5 | Normal | 
| 3 mo | 3.6 | Not done | |
| 14 | Baseline | 1.9 | Normal | 
| 1 mo | 0.7 | Normal | |
| 2 mo | 0.9 | Not done | |
| 15 | Baseline | 2.0 | Desaturation 3% and lactate increase 0.8-2.4 | 
| 2 mo | 1.7 | Normal | |
| 3 mo | 1.6 | Not done | |
| 5 mo | 1.7 | Not done | |
| 16 | Baseline | 1.5 | Normal | 
| 6 mo | 1.4 | Normal | |
| 17 | Baseline | 0.5 | Normal | 
| 6 mo | 0.4 | Not done | |
| 18 | Baseline | 2.8 | Not done | 
| 4 mo | 1.8 | Not done |