Table 2.

Pre- and postdesmopressin clinical laboratory values for homozygous family members

Laboratory valuesIII-1III-2 (IC)
Base-line VWF:Ag (IU/mL) 0.26 0.20 
Peak VWF:Ag (IU/mL) 0.79 0.67 
VWF:Ag half-life (hours) 6.41 4.20 
Base-line VWF:GP1bM (IU/mL) 0.16 0.10 
Peak VWF:GP1bM (IU/mL) 0.72 0.64 
VWF:GP1bM half-life (hours) 4.27 2.40 
Base-line FVIII:C (IU/mL) 0.05 0.04 
Peak FVIII:C (IU/mL) 0.62 0.61 
FVIII:C half-life (IU/mL) 1.90 1.05 
Laboratory valuesIII-1III-2 (IC)
Base-line VWF:Ag (IU/mL) 0.26 0.20 
Peak VWF:Ag (IU/mL) 0.79 0.67 
VWF:Ag half-life (hours) 6.41 4.20 
Base-line VWF:GP1bM (IU/mL) 0.16 0.10 
Peak VWF:GP1bM (IU/mL) 0.72 0.64 
VWF:GP1bM half-life (hours) 4.27 2.40 
Base-line FVIII:C (IU/mL) 0.05 0.04 
Peak FVIII:C (IU/mL) 0.62 0.61 
FVIII:C half-life (IU/mL) 1.90 1.05 
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