Table 1.

PNSs associated with lymphomas

Syndrome/presentationAntibodyType of lymphomaPrognosis/ recovery
Cerebellar degeneration Anti-Tr HL Improvement possible 
Limbic encephalitis (Ophelia syndrome) Anti-mGLU5
Anti-Ma2 
HL HL, NHL Full recovery possible 
Myelopathy None HL, NHL Improvement possible 
Opsoclonus-myoclonus None NHL Improvement unlikely 
Stiff-person syndrome None, may have coexisting anti-GAD65 HL Improvement possible 
Sensorimotor neuronopathy None HL Improvement rarely noted 
Myasthenia gravis AChR HL, NHL Improvement expected; prognosis dependent on the prognosis of lymphoma 
Dermatomyositis p155 NHL Improvement possible but poor prognosis 
Syndrome/presentationAntibodyType of lymphomaPrognosis/ recovery
Cerebellar degeneration Anti-Tr HL Improvement possible 
Limbic encephalitis (Ophelia syndrome) Anti-mGLU5
Anti-Ma2 
HL HL, NHL Full recovery possible 
Myelopathy None HL, NHL Improvement possible 
Opsoclonus-myoclonus None NHL Improvement unlikely 
Stiff-person syndrome None, may have coexisting anti-GAD65 HL Improvement possible 
Sensorimotor neuronopathy None HL Improvement rarely noted 
Myasthenia gravis AChR HL, NHL Improvement expected; prognosis dependent on the prognosis of lymphoma 
Dermatomyositis p155 NHL Improvement possible but poor prognosis 
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